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MJFF Publications

5351 - 5375 of 6433 Results
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  • Summary Details
    OPEN
    Title: Loss‐of‐Function Variants in HOPS Complex Genes VPS16 and VPS41 Cause Early Onset Dystonia Associated with Lysosomal Abnormalities
    Journal Name: Annals of Neurology
    Publisher: Wiley
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1002/ana.25879
    Citation Count: 93
  • Summary Details
    OPEN
    Title: LRRK2 is a negative regulator of Mycobacterium tuberculosis phagosome maturation in macrophages
    Journal Name: The EMBO Journal
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.15252/embj.201798694
    Citation Count: 164
  • Summary Details
    OPEN
    Title: Autosomal recessive VWA1-related disorder: comprehensive analysis of phenotypic variability and genetic mutations
    Journal Name: Brain Communications
    Publisher: Oxford University Press (OUP)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by, cc-by
    DOI - Digital Object Identifier: 10.1093/braincomms/fcae377
    Citation Count: 0
  • Summary Details
    OPEN
    Title: Proximity extension assay testing reveals novel diagnostic biomarkers of atypical parkinsonian syndromes
    Journal Name: Journal of Neurology, Neurosurgery & Psychiatry
    Publisher: BMJ
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1136/jnnp-2018-320151
    Citation Count: 50
  • Summary Details
    OPEN
    Title: Pathological structural conversion of α-synuclein at the mitochondria induces neuronal toxicity
    Journal Name: Nature Neuroscience
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by, cc-by
    DOI - Digital Object Identifier: 10.1038/s41593-022-01140-3
    Citation Count: 172
  • Summary Details
    OPEN
    Title: Post-mortem ventricular cerebrospinal fluid cell-free-mtDNA in neurodegenerative disease
    Journal Name: Scientific Reports
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1038/s41598-020-72190-5
    Citation Count: 22
  • Summary Details
    OPEN
    Title: A Comparative Study of High-Contrast Fluorescence Lifetime Probes for Imaging Amyloid in Tissue
    Journal Name: The Journal of Physical Chemistry B
    Publisher: American Chemical Society (ACS)
    Publication Date:
    Open Access(OA) Status: OPEN
    License:
    DOI - Digital Object Identifier: 10.1021/acs.jpcb.1c07762
    Citation Count: 6
  • Summary Details
    OPEN
    Title: The effect of LRRK2 loss-of-function variants in humans
    Journal Name: Nature Medicine
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1038/s41591-020-0893-5
    Citation Count: 103
  • Summary Details
    OPEN
    Title: Lunapark deficiency leads to an autosomal recessive neurodevelopmental phenotype with a degenerative course, epilepsy and distinct brain anomalies
    Journal Name: Brain Communications
    Publisher: Oxford University Press (OUP)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1093/braincomms/fcad222
    Citation Count: 4
  • Summary Details
    OPEN
    Title: Short hydrogen bonds enhance nonaromatic protein-related fluorescence
    Journal Name: Proceedings of the National Academy of Sciences
    Publisher: Proceedings of the National Academy of Sciences
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1073/pnas.2020389118
    Citation Count: 39
  • Summary Details
    OPEN
    Title: Molecular Mechanisms of Cationic Fusogenic Liposome Interactions with Bacterial Envelopes
    Journal Name: Journal of the American Chemical Society
    Publisher: American Chemical Society (ACS)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1021/jacs.3c11463
    Citation Count: 28
  • Summary Details
    OPEN
    Title: Alzheimer's disease pathology explains association between dementia with Lewy bodies and APOE‐ε4/TOMM40 long poly‐T repeat allele variants
    Journal Name: Alzheimer's & Dementia: Translational Research & Clinical Interventions
    Publisher: Wiley
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by-nc-nd
    DOI - Digital Object Identifier: 10.1016/j.trci.2019.08.005
    Citation Count: 17
  • Summary Details
    OPEN
    Title: powerEQTL: an R package and shiny application for sample size and power calculation of bulk tissue and single-cell eQTL analysis
    Journal Name: Bioinformatics
    Publisher: Oxford University Press (OUP)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1093/bioinformatics/btab385
    Citation Count: 27
  • Summary Details
    OPEN
    Title: L-dopa responsiveness in early Parkinson's disease is associated with the rate of motor progression
    Journal Name: Parkinsonism & Related Disorders
    Publisher: Elsevier BV
    Publication Date:
    Open Access(OA) Status: OPEN
    License:
    DOI - Digital Object Identifier: 10.1016/j.parkreldis.2019.05.022
    Citation Count: 28
  • Summary Details
    OPEN
    Title: Intracellular Aβ42 Aggregation Leads to Cellular Thermogenesis
    Journal Name: Journal of the American Chemical Society
    Publisher: American Chemical Society (ACS)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1021/jacs.2c03599
    Citation Count: 23
  • Summary Details
    OPEN
    Title: Millisecond Hydrogen/Deuterium-Exchange Mass Spectrometry Approach to Correlate Local Structure and Aggregation in α-Synuclein
    Journal Name: Analytical Chemistry
    Publisher: American Chemical Society (ACS)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1021/acs.analchem.2c03183
    Citation Count: 20
  • Summary Details
    OPEN
    Title: ARSA variants in α-synucleinopathies
    Journal Name: Brain
    Publisher: Oxford University Press (OUP)
    Publication Date:
    Open Access(OA) Status: OPEN
    License:
    DOI - Digital Object Identifier: 10.1093/brain/awz340
    Citation Count: 19
  • Summary Details
    OPEN
    Title: Mitophagy bridges glucose metabolism, inflammation and neuroprotection in astrocytes
    Journal Name: Autophagy
    Publisher: Informa UK Limited
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1080/15548627.2026.2623987
    Citation Count: 0
  • Summary Details
    OPEN
    Title: B lymphocyte responses in Parkinson’s disease and their possible significance in disease progression
    Journal Name: Brain Communications
    Publisher: Oxford University Press (OUP)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1093/braincomms/fcad060
    Citation Count: 23
  • Summary Details
    OPEN
    Title: Label-Free Characterization of Amyloids and Alpha-Synuclein Polymorphs by Exploiting Their Intrinsic Fluorescence Property
    Journal Name: Analytical Chemistry
    Publisher: American Chemical Society (ACS)
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by-nc-nd
    DOI - Digital Object Identifier: 10.1021/acs.analchem.1c05651
    Citation Count: 17
  • Summary Details
    OPEN
    Title: Optical Structural Analysis of Individual α‐Synuclein Oligomers
    Journal Name: Angewandte Chemie International Edition
    Publisher: Wiley
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1002/anie.201710779
    Citation Count: 42
  • Summary Details
    OPEN
    Title: The Anthelmintic Drug Niclosamide and Its Analogues Activate the Parkinson's Disease Associated Protein Kinase PINK1
    Journal Name: ChemBioChem
    Publisher: Wiley
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1002/cbic.201700500
    Citation Count: 52
  • Summary Details
    OPEN
    Title: Parkinson’s disease neurons exhibit alterations in mitochondrial quality control proteins
    Journal Name: npj Parkinson's Disease
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by, cc-by
    DOI - Digital Object Identifier: 10.1038/s41531-023-00564-3
    Citation Count: 19
  • Summary Details
    OPEN
    Title: Upregulating β-hexosaminidase activity in rodents prevents α-synuclein lipid associations and protects dopaminergic neurons from α-synuclein-mediated neurotoxicity
    Journal Name: Acta Neuropathologica Communications
    Publisher: Springer Science and Business Media LLC
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1186/s40478-020-01004-6
    Citation Count: 19
  • Summary Details
    OPEN
    Title: Comparison of Patient and Expert Perceptions of the Attainment of Research Milestones in Parkinson's Disease
    Journal Name: Movement Disorders
    Publisher: Wiley
    Publication Date:
    Open Access(OA) Status: OPEN
    License: cc-by
    DOI - Digital Object Identifier: 10.1002/mds.28319
    Citation Count: 4
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